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Review
. 2010 Mar;17(2):181-9.
doi: 10.1053/j.ackd.2009.12.005.

Isolated polycystic liver disease

Qi Qian  1
Affiliations
Review

Isolated polycystic liver disease

Qi Qian. Adv Chronic Kidney Dis. 2010 Mar.

Abstract

Isolated polycystic liver disease (PCLD) is an autosomal dominant disease with genetic and clinical heterogeneity. Apart from liver cysts, it exhibits few extrahepatic manifestations, and the majority of patients with this condition are asymptomatic or subclinical. However, a small fraction of these patients develop acute liver cyst-related complications and/or massive cystic liver enlargement, causing morbidity and mortality. Currently, the management for symptomatic PCLD is centered on palliating symptoms and treating complications.

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Figures

Figure 1
Figure 1
Transverse CT scan images from a patient with PCLD (1A) and a patient with ADPKD (1B). In PCLD, numerous cysts are confined in the liver, but in ADPKD cysts involve both the liver and kidneys.
See this image and copyright information in PMC

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