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Case Reports
. 2008 Jan;1(1):62-4.
doi: 10.4103/0974-2069.41060.

Arterial tortuosity syndrome: A rare entity

Ashutosh Marwah  1 , Sejal Shah, P V Suresh, Sunita Maheshwari
Affiliations
Case Reports

Arterial tortuosity syndrome: A rare entity

Ashutosh Marwah et al. Ann Pediatr Cardiol. 2008 Jan.

Abstract

We present a 5 month old baby who was referred for an incidental detection of a murmur and was found to have tortuous pulmonary arteries with multiple peripheral pulmonary stenoses and bilateral inguinal hernia pointing towards the diagnosis of arterial tortuosity syndrome.

Keywords: Arterial tortuosity syndrome; tortuous pulmonary arteries.

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Conflict of interest statement

Conflict of Interest: None declared

Figures

Figure 1
Figure 1
Pulmonary artery angiogram in AP view showing tortuous right pulmonary artery with peripheral stenoses. RPA= right pulmonary artery
Figure 2
Figure 2
Pulmonary artery angiogram in AP view showing tortuous left pulmonary artery with stenosis. LPA= left pulmonary artery
Figure 3
Figure 3
Left ventricular angiogram in LAO view showing elongated aortic root and aortic arch. LV= left ventricle
See this image and copyright information in PMC

References

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