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Case Reports
. 2008 Jul;1(2):147-8.
doi: 10.4103/0974-2069.43884.

Primary primitive neuroectodermal tumor: An unusual cause of right ventricular intracavitary obstruction in a child

Ajit Thachil  1 , Anita Saxena, Ujjwal K Choudhary, Ruma Ray
Affiliations
Case Reports

Primary primitive neuroectodermal tumor: An unusual cause of right ventricular intracavitary obstruction in a child

Ajit Thachil et al. Ann Pediatr Cardiol. 2008 Jul.

Abstract

A six-year-old boy presented with a brief history suggestive of right heart failure. Investigations revealed a mass filling almost the entire right ventricle. Palliative resection of the mass was done. The operative specimen revealed a primary primitive neuroectodermal tumor of the heart, the first of its kind reported in the pediatric age group.

Keywords: Cardiac masses; cardiac failure; neuroectodermal tumor.

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Conflict of interest statement

Conflict of Interest: None declared

Figures

Figure 1
Figure 1
Echocardiogram in apical 4 – chamber view; RA, right atrium; RV, right ventricle; LV, left ventricle
Figure 2
Figure 2
Extension of the tumor into the RVOT showing the tumor filling the right ventricle in parasternal short axis view; RVOT, right ventricular outflow tract
Figure 3
Figure 3
Histology – H and E stain showing a small round cell tumor
Figure 4
Figure 4
Immunocytochemistry – tumor cells show membrane positivity for MIC-2 (CD99), suggesting a primitive neuroectodermal tumor
See this image and copyright information in PMC

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