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Case Reports
. 2013 Mar;32 Suppl 1(Suppl 1):S41-2.
doi: 10.1007/s10067-010-1428-0. Epub 2010 Mar 28.

Complete remission of coronary vasculitis in Churg-Strauss Syndrome by prednisone and cyclophosphamide

Niels P Riksen  1 , Helmut Gehlmann, Annemarie E Brouwer, Marcel van Deuren
Affiliations
Case Reports

Complete remission of coronary vasculitis in Churg-Strauss Syndrome by prednisone and cyclophosphamide

Niels P Riksen et al. Clin Rheumatol. 2013 Mar.

Abstract

The heart is involved in up to 50% of all patients with Churg-Strauss syndrome, but vasculitis of the coronary arteries has only been rarely documented. We present a young patient with severe coronary aneurysms and stenotic lesions due to a Churg-Strauss vasculitis. Prompt therapy with prednisone and cyclophosphamide resulted in the complete resolution of all lesions.

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Figures

Fig. 1
Fig. 1
Left coronary angiogram in right inferior oblique view before (a) and after (b) 1 year of immunosuppressive therapy with prednisone and cyclophosphamide. Before the treatment, there were two prominent aneurysms in the intermediate branch and one large aneurysm proximally in the obtuse marginal branch (a, indicated by white arrows) in addition to diffuse wall irregularities in all branches. After the treatment, all these lesions have disappeared completely (b)
See this image and copyright information in PMC

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