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. 2010 Mar;26(3):e80-97.
doi: 10.1016/s0828-282x(10)70355-x.

Canadian Cardiovascular Society 2009 Consensus Conference on the management of adults with congenital heart disease: outflow tract obstruction, coarctation of the aorta, tetralogy of Fallot, Ebstein anomaly and Marfan's syndrome

Candice K Silversides  1 , Marla Kiess, Luc Beauchesne, Timothy Bradley, Michael Connelly, Koichiro Niwa, Barbara Mulder, Gary Webb, Jack Colman, Judith Therrien
Affiliations

Canadian Cardiovascular Society 2009 Consensus Conference on the management of adults with congenital heart disease: outflow tract obstruction, coarctation of the aorta, tetralogy of Fallot, Ebstein anomaly and Marfan's syndrome

Candice K Silversides et al. Can J Cardiol. 2010 Mar.

Abstract
in English, French

With advances in pediatric cardiology and cardiac surgery, the population of adults with congenital heart disease (CHD) has increased. In the current era, there are more adults with CHD than children. This population has many unique issues and needs. Since the 2001 Canadian Cardiovascular Society Consensus Conference report on the management of adults with CHD, there have been significant advances in the field of adult CHD. Therefore, new clinical guidelines have been written by Canadian adult CHD physicians in collaboration with an international panel of experts in the field. Part II of the guidelines includes recommendations for the care of patients with left ventricular outflow tract obstruction and bicuspid aortic valve disease, coarctation of the aorta, right ventricular outflow tract obstruction, tetralogy of Fallot, Ebstein anomaly and Marfan's syndrome. Topics addressed include genetics, clinical outcomes, recommended diagnostic workup, surgical and interventional options, treatment of arrhythmias, assessment of pregnancy risk and follow-up requirements. The complete document consists of four manuscripts that are published online in the present issue of The Canadian Journal of Cardiology. The complete document and references can also be found at www.ccs.ca or www.cachnet.org.

Étant donné les progrès de la cardiologie pédiatrique et de la chirurgie cardiaque, la population d’adultes ayant une cardiopathie congénitale (CPC) a augmenté. Il y a maintenant plus d’adultes que d’enfants ayant une CPC. Cette population a de nombreux problèmes et besoins uniques. Depuis le rapport de la conférence consensuelle 2001 de la Société canadienne de cardiologie sur la prise en charge des adultes ayant une CPC, on constate d’importantes avancées dans le domaine des CPC chez les adultes. Par conséquent, de nouvelles lignes directrices cliniques ont été rédigées par des médecins canadiens s’occupant des CPC chez les adultes, en collaboration avec un groupe d’experts internationaux dans le domaine. La partie II des lignes directrices contient des recommandations sur les soins aux patients ayant une obstruction de la chambre de chasse du ventricule gauche et une bicuspidie valvulaire aortique, une coarctation de l’aorte, une obstruction de la chambre de chasse du ventricule droit, une tétralogie de Fallot, une maladie d’Ebstein et un syndrome de Marfan. Les sujets abordés incluent la génétique, les issues cliniques, les bilans diagnostiques recommandés, les possibilités chirurgicales et d’intervention, le traitement des arythmies, l’évaluation des risques de la grossesse et de la contraception et les recommandations de suivi. Le document complet se compose de quatre manuscrits publiés par voie électronique dans le présent numéro du Journal canadien de cardiologie. Le document complet et les références figurent également aux adresses www.ccs.ca et www.cachnet.org.

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References

    1. Morris CA, Mervis CB. Williams syndrome and related disorders. Annu Rev Genomics Hum Genet. 2000;1:461–84. - PubMed
    1. Nickerson E, Greenberg F, Keating MT, McCaskill C, Shaffer LG. Deletions of the elastin gene at 7q11.23 occur in approximately 90% of patients with Williams syndrome. Am J Hum Genet. 1995;56:1156–61. - PMC - PubMed
    1. Aboulhosn J, Child JS. Left ventricular outflow obstruction: Subaortic stenosis, bicuspid aortic valve, supravalvar aortic stenosis, and coarctation of the aorta. Circulation. 2006;114:2412–22. - PubMed
    1. Fedak PW, Verma S, David TE, Leask RL, Weisel RD, Butany J. Clinical and pathophysiological implications of a bicuspid aortic valve. Circulation. 2002;106:900–4. - PubMed
    1. Beppu S, Suzuki S, Matsuda H, Ohmori F, Nagata S, Miyatake K. Rapidity of progression of aortic stenosis in patients with congenital bicuspid aortic valves. Am J Cardiol. 1993;71:322–7. - PubMed

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