Primary small bowel liposarcoma (atypical lipomatous tumour) with myogenic differentiation

Abstract

Primary small intestinal liposarcomas originating in the small bowel are uncommon with a generally poor prognosis due to the advanced stage at the time of diagnosis. We describe a case of primary small bowel dedifferentiated liposarcoma presenting as a solid mass in the right iliac fossa. The current case is unusual as the tumour seemingly originated from the bowel and the well-differentiated component was seen extensively infiltrating the bowel wall including the small bowel submucosa.

Figure 1

(a) A solid mass in the right iliac fossa not attached to the bowel wall, (b), (c) well-differentiated liposarcoma infiltrating the submucosa, (d), (e), and (f) dedifferentiated component infiltrating the small bowel, and (g), (h) well-differentiated liposarcoma at the small bowel resection margins.