Review
doi: 10.1007/s00247-010-1793-5.
Epub 2010 Aug 17.
Update on congenital nephrotic syndromes and the contribution of US
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- PMID: 20714714
- DOI: 10.1007/s00247-010-1793-5
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Review
Update on congenital nephrotic syndromes and the contribution of US
Pediatr Radiol.
2011 Jan.
Abstract
The clinical classification of nephrotic syndrome (NS) is based on age at presentation. However, this classification is arbitrary because the majority of early onset NS has a genetic origin and has a widespread age of onset (from fetal life to several years). The aims of this review are to illustrate the knowledge accumulated on congenital nephrotic syndrome (CNS) in terms of genetics, classification, findings at histology and US-based on a review of the literature.
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