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. 1990 Feb;40(2):293-5.
doi: 10.1212/wnl.40.2.293.

Extrapyramidal involvement in Rett's syndrome

P M FitzGerald  1 , J Jankovic, D G Glaze, R Schultz, A K Percy
Affiliations

Extrapyramidal involvement in Rett's syndrome

P M FitzGerald et al. Neurology. 1990 Feb.

Abstract

Extrapyramidal dysfunction is poorly characterized in Rett's syndrome, a neurodegenerative disorder in girls. We studied the motor and behavioral findings in 32 Rett's syndrome patients, 21 months to 30 years old. In addition to the typical stereotyped movements and scoliosis, other motor disturbances included bruxism, sialorrhea, ocular deviations, parkinsonian findings, dystonia, myoclonus, and athetosis. The types of movement disorders seemed to be age-related, with the hyperkinetic disorders occurring in the younger patients and the bradykinetic disorders occurring more frequently in the older patients.

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Comment in

  • Rett's syndrome.
    Kerr AM, Stephenson JB. Kerr AM, et al. Neurology. 1990 Nov;40(11):1804. doi: 10.1212/wnl.40.11.1804. Neurology. 1990. PMID: 2234445 No abstract available.

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