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. 2010 Oct;17(4):379-81.
doi: 10.4103/0974-9233.71591.

Progressive posterior lenticonus in a patient with alport syndrome

Ammar M Al-Mahmood  1 , Samar A Al-Swailem, Abdulrahman Al-Khalaf, Ghada Y Al-Binali
Affiliations

Progressive posterior lenticonus in a patient with alport syndrome

Ammar M Al-Mahmood et al. Middle East Afr J Ophthalmol. 2010 Oct.

Abstract

We report a rare case of Alport syndrome with progressive posterior lenticonus. A 24-year-old male presented to our tertiary eye care center with history of poor vision. At initial presentation, the patient had bilateral anterior lenticonus, posterior subcapsular cataract, and renal failure. The patient was diagnosed with Alport syndrome based on a positive family history of the disease and clinical findings. Further examination revealed progressive posterior lenticonus that was not present initially. The presence of such finding is important because it influences the surgical approach to avoid complications during cataract surgery.

Keywords: Alport Syndrome; Anterior Lenticonus; Posterior Lenticonus; X-linked Disease.

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Conflict of interest statement

Conflict of Interest: None declared

Figures

Figure 1
Figure 1
Anterior lenticonus in the right eye in a patient with Alport syndrome
Figure 2
Figure 2
Oil droplet sign with retro-illumination in a patient with Alport syndrome
Figure 3
Figure 3
Posterior lenticonus in the right eye in a patient with Alport syndrome
See this image and copyright information in PMC

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