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. 2011 Feb;60(2):124-7.
doi: 10.4097/kjae.2011.60.2.124. Epub 2011 Feb 25.

Anesthetic experience of a patient with Ohtahara syndrome -A case report-

Eun Mi Choi  1 , Kyeong Tae Min, Jin Sun Cho, Seung Ho Choi
Affiliations

Anesthetic experience of a patient with Ohtahara syndrome -A case report-

Eun Mi Choi et al. Korean J Anesthesiol. 2011 Feb.

Abstract

Ohtahara syndrome (OS) is a rare epileptic encephalopathy that is characterized by an abnormal electroencephalogram (EEG) and intractable seizures in the neonatal and early infantile period. The patient of this reported case was delivered normally at 39 weeks of gestation without any complication. One week after birth, seizures that were refractory to anticonvulsants started with repetitive clustered tonic spasms. The child had no abnormal findings on the initial laboratory investigations. But he was diagnosed with OS according to the frequent tonic spasms, an abnormal EEG pattern of suppression-burst and magnetic resonance imaging of cortical dysplasia. He was planned to undergo an operation for brain lesion. This report describes our experience with the general anesthetic management when we performed craniotomy and right hemispherotomy for a patient with OS.

Keywords: Infantile epileptic syndrome; Ohtahara syndrome; Suppression-burst.

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Figures

Fig. 1
Fig. 1
Magnetic resonance imaging shows a structural abnormality of cortical dysplasia in the right temporal (A) and parietal (B) lobes.
Fig. 2
Fig. 2
The electroencephalogram shows excessively asynchronous and discontinuous rhythms, the so called suppression-burst patterns, on the right hemisphere.
See this image and copyright information in PMC

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