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Review
. 2011 Mar 21;17(11):1410-5.
doi: 10.3748/wjg.v17.i11.1410.

Portal ductopathy: clinical importance and nomenclature

Yusuf Bayraktar  1
Affiliations
Review

Portal ductopathy: clinical importance and nomenclature

Yusuf Bayraktar. World J Gastroenterol. .

Abstract

Non-cirrhotic portal hypertension (PHT) accounts for about 20% of all PHT cases, portal vein thrombosis (PVT) resulting in cavernous transformation being the most common cause. All known complications of PHT may be encountered in patients with chronic PVT. However, the effect of this entity on the biliary tree and pancreatic duct has not yet been fully established. Additionally, a dispute remains regarding the nomenclature of common bile duct abnormalities which occur as a result of chronic PVT. Although many clinical reports have focused on biliary abnormalities, only a few have evaluated both the biliary and pancreatic ductal systems. In this review the relevant literature evaluating the effect of PVT on both ductal systems is discussed, and findings are considered with reference to results of a prominent center in Turkey, from which the term "portal ductopathy" has been put forth to replace "portal biliopathy".

Keywords: Congenital hepatic fibrosis; Non-cirrhotic portal hypertension; Portal biliopathy; Portal double ductopathy; Portal ductopathy; Portal hypertension; Portal vein cavernous transformation; Portal vein thrombosis.

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Figures

Figure 1
Figure 1
Endoscopic retrograde cholangiopancreatography showing typical portal ductopathy with external compression of the common bile duct (white arrow) leading to almost complete obstruction and dilatation of the intrahepatic bile ducts. The pancreatic duct is atrophic (black arrow).
See this image and copyright information in PMC

References

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