Skip to main page content
U.S. flag

An official website of the United States government

Dot gov

The .gov means it’s official.
Federal government websites often end in .gov or .mil. Before sharing sensitive information, make sure you’re on a federal government site.

Https

The site is secure.
The https:// ensures that you are connecting to the official website and that any information you provide is encrypted and transmitted securely.

Access keys NCBI Homepage MyNCBI Homepage Main Content Main Navigation
. 2009:2009:bcr2006099465b.
doi: 10.1136/bcr.2006.099465b. Epub 2009 Feb 18.

Mid-brain molar tooth sign: expanding the clinical spectrum

J N Panicker  1 , B Jyothi, K P Sreekumar
Affiliations

Mid-brain molar tooth sign: expanding the clinical spectrum

J N Panicker et al. BMJ Case Rep. 2009.
No abstract available

PubMed Disclaimer

Conflict of interest statement

Competing interests: None declared.

Figures

Figure 1
Figure 1. (A) Coronal T1 weighted magnetic resonance images showing superior vermian dysplasia with agenesis of mid and inferior vermian lobules and apposing cerebellar hemispheres (arrows). (B) Transverse T2 weighted image at the level of mid-brain interpeduncular fossa showing classical molar tooth sign (arrow) and triangular shape of the fourth ventricle (arrowhead). (C) Transverse T2 weighted image at the level of the upper pons showing a dilated fourth ventricle with bat-wing morphology (arrow). (D) Mid-sagittal T1 weighted image showing a high position of the fourth ventricle (arrow) and curved roof (arrowhead).
See this image and copyright information in PMC

References

    1. Patel S, Barkovich AJ. Analysis and classification of cerebellar malformations. Am J Neuroradiol. 2002;23:1074–87. - PMC - PubMed
    1. Gleeson JG, Keeler LC, Parisi MA, et al. Molar tooth sign of the midbrain-hindbrain junction: occurrence in multiple distinct syndromes. Am J Med Genet. 2004;125A:125–34. - PubMed
    1. Romano S, Boddaert N, Desguerre I, et al. Molar tooth sign and superior vermian dysplasia: a radiological, clinical, and genetic study. Neuropediatrics. 2006;37:42–5. - PubMed
    1. Satran D, Pierpont ME DobynsWB. Cerebello-oculo-renal syndromes including Arima, Senior-Loken and COACH syndromes: more than just variants of Joubert syndrome. Am J Med Genet. 1999;86:459–69. - PubMed

LinkOut - more resources