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Review
. 2011;16(10):1388-96.
doi: 10.1634/theoncologist.2011-0120. Epub 2011 Sep 20.

Familial pediatric endocrine tumors

Sarinda Millar  1 , Lisa Bradley, Deirdre E Donnelly, Dennis Carson, Patrick J Morrison
Affiliations
Review

Familial pediatric endocrine tumors

Sarinda Millar et al. Oncologist. 2011.

Abstract

Pediatric endocrine tumors are rare but have fairly characteristic presentations. We describe an approach to diagnosis and management of five of the most common presentations including gonadoblastoma, paraganglioma, medullary thyroid cancer, adrenal cancer, and pituitary adenoma. Genetic testing can aid in the early detection and prevention and management of tumors in patients and in other family members.

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Conflict of interest statement

Disclosures

Sarinda Millar: None; Lisa Bradley: None; Deirdre E. Donnelly: None; Dennis Carson: None; Patrick J. Morrison: None.

Section Editor Herbert Chen discloses no financial relationships.

Section Editor Stan Sidhu discloses no financial relationships.

Reviewers “A” and “B” disclose no relevant financial relationships.

The content of this article has been reviewed by independent peer reviewers to ensure that it is balanced, objective, and free from commercial bias. On the basis of disclosed information, no conflicts of interest were identified.

Figures

Figure 1.
Figure 1.
Lymphedema of wrists and dorsum of hand classically found in Turner syndrome neonates.
Figure 2.
Figure 2.
Cut surface of a resected pheochromocytoma.
Figure 3.
Figure 3.
Focal medullary carcinoma in situ.
Figure 4.
Figure 4.
Magnetic resonance imaging scan of adrenal tumor.
Figure 5.
Figure 5.
Angiogram of neck showing carotid body tumor (paraganglioma).
Figure 6.
Figure 6.
Café-au-lait spots.
Figure 7.
Figure 7.
Mucosal neuromas of the tongue and prominent lips in multiple endocrine neoplasia 2B.
See this image and copyright information in PMC

References

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