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. 2011 Jan-Mar;1(1):122-4.
doi: 10.4103/2045-8932.78096.

Diagnostic and therapeutic algorithm for pulmonary arterial hypertension

Affiliations

Diagnostic and therapeutic algorithm for pulmonary arterial hypertension

Ankit A Desai et al. Pulm Circ. 2011 Jan-Mar.
No abstract available

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Conflict of interest statement

Conflict of Interest: None declared.

Figures

Figure 1
Figure 1
PAH diagnostic algorithm. (ABG - Arterial blood gas; ALK-1 - Activin-receptor-like kinase; ANA - Anti-nuclear antibodies; BMPR2 - Bone morphogenetic protein receptor 2; CHD - Congenital heart disease; CMR - Cardiac magnetic resonance; CT - Computed tomography; CTD - Connective tissue disease; ECG - Electrocardiogram; FMHx - Family medical history; HHT - Hereditary hemorrhagic telangiectasia; HRCT - High-resolution computed tomography; LFTs - Liver function tests; LH - Left heart; PAP - Pulmonary arterial pressure; LVEDP - Left ventricular end-diastolic pressure; PAH - Pulmonary arterial hypertension; IPAH - Idiopathic pulmonary arterial hypertension; PCH - Pulmonary capillary hemangiomatosis; PE - Pulmonary thromboembolic disease; PFT - Pulmonary function test; PH - Pulmonary hypertension; PVOD - Pulmonary venoocclusive disease; RHC - Right heart catheterization; TEE - Transesophageal echocardiography; TTE - Transthoracic echocardiography; US - Ultrasonography; V/Q - Ventilation/perfusion lung scan; WHO - World Health Organization)
Figure 2
Figure 2
PAH treatment algorithm. (PAH - Pulmonary arterial hypertension; FC - Functional class; ERA - Endothelin receptor antagonist; PDE-I - Phosphodiesterase type 5 inhibitor; IV - Intravenous; PO - Oral; SC - Subcutaneous; NA - Not approved; WHO - World Health Organization; PAP - Pulmonary arterial pressure; RCT - Randomized controlled trial. Strength of recommendation: A - Strong recommendation; B - Moderate recommendation; C - Weak recommendation; D - Negative recommendation; E/A - Strong recommendation on the basis of expert opinion only; E/B - Moderate recommendation on the basis of expert opinion only; E/C - Weak recommendation on the basis of expert opinion only; E/D - Negative recommendation on the basis of expert opinion only)

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