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Review
. 1990 Jun-Jul;47(6):441-4.

[Proteus syndrome]

[Article in French]
J J Benichou  1 , B Labrune, A Formanek, C Denoix, P Oger
Affiliations
  • PMID: 2206106
Review

[Proteus syndrome]

[Article in French]
J J Benichou et al. Arch Fr Pediatr. 1990 Jun-Jul.

Abstract

Two new cases of Proteus syndrome are reported. This congenital syndrome, first described in 1983, comprises gigantism of extremities, body hemihypertrophy, pigmented nevi and multiple tumors (subcutaneous, lipomas, hamartomas). This syndrome belongs to the same group as Recklinghausen disease, Maffucci or Klippel-Trenaunay syndromes. The prognosis is not well known but mostly depends on functional and psychologic consequences of important deformations.

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