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Case Reports
. 2011 Apr;12(2):74-8.
doi: 10.4103/1995-705X.86019.

Isolated Non-compaction Cardiomyopathy Presented with Ventricular Tachycardia

Virendra C Patil  1 , Harsha V Patil
Affiliations
Case Reports

Isolated Non-compaction Cardiomyopathy Presented with Ventricular Tachycardia

Virendra C Patil et al. Heart Views. 2011 Apr.

Abstract

Non-compaction cardiomyopathy is a recently recognized disorder, based on an arrest in endomyocardial morphogenesis. The disease is characterized by heart failure (both diastolic and systolic), systemic emboli and ventricular arrhythmias. The diagnosis is established by two-dimensional echocardiography. Isolated left ventricular non-compaction cardiomyopathy (IVNC) is an exceedingly rare congenital cardiomyopathy. Only a few cases of this condition have been reported. It is characterized by prominent and excessive trabeculation in a ventricular wall segment, with deep intertrabecular spaces perfused from the ventricular cavity. Echocardiographic findings are important clues for the diagnosis. We report a case of isolated non-compaction of the left ventricular myocardium presented with ventricular tachycardia.

Keywords: IVNC; Isolated non-compaction cardiomyopathy; non-compaction cardiomyopathy; ventricular tachycardia.

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Conflict of interest statement

Conflict of Interest: None declared.

Figures

Figure 1
Figure 1
Transthoracic two-dimensional apical four chamber (AP-4-CH view), parasternal long axis (PLAX) and parasternal short axis (PSAX) images show, isolated non-compaction of left ventricle with multiple trabeculae and intertrabecular recesses in lateral, anterior walls, middle and apical portions of the septum and apex of the left ventricle with severe concentric left ventricular hypertrophy
Figure 2
Figure 2
Transthoracic two-dimensional echocardiogram in apical four chamber (AP-4-CH view), parasternal short axis (PSAX) and parasternal long axis (PLAX) shows deep trabeculae and intertrabecular recesses in the lateral, anterior walls, middle and apical portions of the septum and apex of the left ventricle
Figure 3
Figure 3
Two-dimensional echocardiogram in apical four chamber zoom view (AP-4-CH view), parasternal long axis (PLAX) and parasternal short axis (PSAX) shows color Doppler images at the level of both ventricles that demonstrate the noncompacted:compacted wall ratio and how the color enters the intertrabecular recesses
See this image and copyright information in PMC

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