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Case Reports
. 2012 Jan;85(1009):93-5.
doi: 10.1259/bjr/13687494.

Characteristic CT appearance of lung cysts prompting the diagnosis of a rare genodermatosis

H Rahbar  1 , Z Tavakkol, P Bhargava
Affiliations
Case Reports

Characteristic CT appearance of lung cysts prompting the diagnosis of a rare genodermatosis

H Rahbar et al. Br J Radiol. 2012 Jan.
No abstract available

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Figures

Figure 1
Figure 1
(a) Axial CT image at the level of upper lobes showing two small thin-walled cysts (arrows). (b) Multiple cysts of varying sizes are shown, the largest of which are seen in left lower lobe anterior along inferior major fissure. Cysts on either side abut and encase lower lobe pulmonary artery branches (arrows). Intervening lung parenchyma is normal. (c) Coronal image reconstruction shows multiple peripheral cysts with a medial basilar predominance (arrows).
Figure 2
Figure 2
A papule from the patient's right posterior auricular area was biopsied, and pathology shows a fibrofolliculoma. Note the finger-like projections from a dilated follicle extending into a fibrotic stroma.
See this image and copyright information in PMC

References

    1. Birt AR, Hogg GR, Dube WJ. Hereditary multiple fibrofolliculomas with trichodiscomas and acrochordons. Arch Dermatol 1977;113:1674–7 - PubMed
    1. Toro JR, Glenn G, Duray P, Darling T, Weirich G, Zbar B, et al. Birt-Hogg-Dube syndrome: a novel marker of kidney neoplasia. Arch Dermatol 1999;135:1195–202 - PubMed
    1. Tobino K, Gunji Y, Kurihara M, Kunogi M, Koike K, Tomiyama N, et al. Characteristics of pulmonary cysts in Birt-Hogg-Dube syndrome: thin-section CT findings of the chest in 12 patients. Eur J Radiol 2011;77:403–9 - PubMed
    1. Toro JR, Pautler SE, Stewart L, Glenn GM, Weinreich M, Toure O, et al. Lung cysts, spontaneous pneumothorax, and genetic associations in 89 families with Birt-Hogg-Dube syndrome. Am J Respir Crit Care Med 2007;175:1044–53 - PMC - PubMed
    1. Toro JR. Birt-Hogg-Dubé Syndrome. In: Pagon RA, BT, Dolan CR, Stephens K, editor. GeneReviews (Internet). Seattle, WA: 2006 (updated 2008). Available from: http://www.ncbi.nlm.nih.gov/books/NBK1522/

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