Skip to main page content
U.S. flag

An official website of the United States government

Dot gov

The .gov means it’s official.
Federal government websites often end in .gov or .mil. Before sharing sensitive information, make sure you’re on a federal government site.

Https

The site is secure.
The https:// ensures that you are connecting to the official website and that any information you provide is encrypted and transmitted securely.

Access keys NCBI Homepage MyNCBI Homepage Main Content Main Navigation
. 2011;9(4):191-3.
doi: 10.1089/lrb.2011.0023.

Pulmonary lymphangiomatosis

Melissa N Satria  1 , Gustavo Pacheco-Rodriguez, Joel Moss
Affiliations

Pulmonary lymphangiomatosis

Melissa N Satria et al. Lymphat Res Biol. 2011.

Abstract

Lymphangiomatosis is a rare disease characterized by diffuse infiltration of lymphangiomas in the lung, bone, and other tissues. Due to its rarity, the spectrum of lymphangiomatosis is beginning to be elucidated based on case reports. The limited pathological, radiological, and clinical studies have shed light on this disease. Treatments have been tested in unblinded manner with promising results; however, further understanding of the pathogenesis of disease, as well as its natural history, is needed to facilitate drug development.

PubMed Disclaimer

References

    1. Faul JL, et al. Thoracic lymphangiomas, lymphangiectasis, lymphangiomatosis, and lymphatic dysplasia syndrome. Am J Respir Crit Care Med. 2000;161:1037–1046. - PubMed
    1. Hilliard RI. McKendry JB. Phillips MJ. Congenital abnormalities of the lymphatic system: A new clinical classification. Pediatrics. 1990;86:988–994. - PubMed
    1. Tazelaar HD, et al. Diffuse pulmonary lymphangiomatosis. Hum Pathol. 1993;24:1313–1322. - PubMed
    1. Alvarez OA. Kjellin I. Zuppan CW. Thoracic lymphangiomatosis in a child. J Pediatr Hematol Oncol. 2004;26:136–141. - PubMed
    1. Caballero Y. Perez D. Cano JR. Diffuse pulmonary lymphangiomatosis with mediastinal affectation. Arch Bronconeumol. 2011;47:474–475. - PubMed

Publication types

Supplementary concepts