Ectopic ACTH syndrome due to pheochromocytoma: case report and review of the literature
- PMID: 222080
- PMCID: PMC2595434
Ectopic ACTH syndrome due to pheochromocytoma: case report and review of the literature
Abstract
A 51-year-old female was diagnosed preoperatively to have a pheochromocytoma producing ACTH. This diagnosis was based upon her paroxysmal hypertension, hyperpigmentation, and hypokalemia. Elevated levels of serum and urine corticosteroids, plasma ACTH, urinary VMA, and catecholamines fell after a right adrenal pheochromocytoma was removed. Subsequently this tumor was found to have a high content of ACTH. Review of the literature indicates a mortality rate of 57% for this syndrome. Proper preoperative recognition and management can result in total cure.
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