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Review
. 2012 Jan-Feb;18(1):59-61.
doi: 10.4103/1319-3767.91728.

Caroli's syndrome in a post renal transplant patient: case report and review of the literature

Muhammad Z Bawany  1 , Osama Alaradi, Ali Nawras
Affiliations
Review

Caroli's syndrome in a post renal transplant patient: case report and review of the literature

Muhammad Z Bawany et al. Saudi J Gastroenterol. 2012 Jan-Feb.

Abstract

Caroli's syndrome is characterized by bile duct ectasia in association with hepatic fibrosis. It is usually transmitted in an autosomal recessive fashion and has been well documented to be associated with autosomal recessive polycystic kidney disease and occasionally with autosomal dominant polycystic kidney disease. However, there has been only few case reports published with Caroli's syndrome diagnosed postrenal transplantation.

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Conflict of interest statement

Conflict of Interest: None declared.

Figures

Figure 1
Figure 1
CAT scan showing saccular dilatation of biliary tree mostly in the right lobe of the liver
Figure 2
Figure 2
ERCP showing diffuse saccular dilatation of biliary tree (left>right)
See this image and copyright information in PMC

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