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Case Reports
. 2011 Oct;2(4):385-9.
doi: 10.4103/0976-237X.91810.

Solitary median maxillary central incisor in association with hemifacial microsomia: A rare case report and review of literature

Ashok Utreja  1 , Syed Naved Zahid, Richa Gupta
Affiliations
Case Reports

Solitary median maxillary central incisor in association with hemifacial microsomia: A rare case report and review of literature

Ashok Utreja et al. Contemp Clin Dent. 2011 Oct.

Abstract

Solitary median maxillary central incisor (SMMCI) is a rare dental anomaly. It is estimated to occur in 1:50,000 live births. The SMMCI tooth differs from the normal central incisor in that the crown form is symmetric and it develops and erupts precisely in the midline of the maxillary dental arch in both primary and permanent dentitions. Presence of SMMCI with hemifacial microsomia (HFM) is a very rare clinical condition. We report a case of HFM in a male of Indian origin who presented with SMMCI in both primary and permanent dentitions. The association of HFM with SMMCI may be due to defective development of neural crest cells and/or lack of space in maxilla.

Keywords: Hemifacial microsomia; anodontia; solitary median maxillary central incisor.

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Conflict of interest statement

Conflict of Interest: None declared.

Figures

Figure 1
Figure 1
Frontal view of the patient at 6 years showing facial asymmetry, indistinct philtrum and SMMCI
Figure 2
Figure 2
Intraoral view showing the presence of SMMCI (primary central incisor) and absence of labial frenum
Figure 3
Figure 3
Intraoral periapical radiograph confirming the presence of SMMCI and intermaxillary suture
Figure 4
Figure 4
Extraoral frontal view at 8 years showing exaggerated asymmetry and retarded growth on the left side
Figure 5
Figure 5
Right lateral view showing normal development
Figure 6
Figure 6
Left lateral view showing stunted growth
Figure 7
Figure 7
Intraoral view at 8 years showing SMMCI (permanent central incisor)
Figure 8
Figure 8
Panoramic radiograph at 8 years of age showing HFM, SMMCI, and delayed eruption on the left side
See this image and copyright information in PMC

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