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Case Reports
. 2012 Jun;21 Suppl 4(Suppl 4):S569-72.
doi: 10.1007/s00586-012-2311-2. Epub 2012 Apr 24.

Currarino's triad diagnosed in an adult woman

Lotte M E Berghauser Pont  1 , Clemens M F Dirven, Ruben Dammers
Affiliations
Case Reports

Currarino's triad diagnosed in an adult woman

Lotte M E Berghauser Pont et al. Eur Spine J. 2012 Jun.

Abstract

Purpose: To report on a female patient diagnosed with Currarino's triad in adulthood.

Case report: This case presents an adult patient with a medical history of a congenital anal atresia, a partial sacral agenesis, and a surgically treated ectopic anus. After a coincidentally observed presacral mass by MRI, due to unexplained constipation later in adulthood, Currarino's triad was suspected in this patient. This triad consists of anorectal malformation(s), sacrococcygeal defects and a presacral mass of various origin. Further investigation confirmed the mass to be a meningocele, and showed a tethered cord and a syrinx.

Conclusions: In (young) patients with anorectal malformations, although having no other symptoms, further examination might be required to exclude Currarino's triad. Importance of early diagnosis and multidisciplinary assessment is recommended to establish adequate treatment if needed.

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Figures

Fig. 1
Fig. 1
Pelvic X-ray Arrow A: the partial sacral agenesis
Fig. 2
Fig. 2
MRI with contrast enhancement. Arrow A: mild syringomyelia. Arrow B: tethered cord with medullary conus at L3–4 level. Arrow C: anterior meningocele
See this image and copyright information in PMC

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Publication types

Supplementary concepts