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Case Reports
. 2012 Apr;3(Suppl 1):S86-91.
doi: 10.4103/0976-237X.95113.

Aesthetic and functional management of a patient with Cornelia de Lange syndrome

Dexton Antony Johns  1 , Dnyanesh L Bhonsale, V Y Shivashanker, Manu Johns
Affiliations
Case Reports

Aesthetic and functional management of a patient with Cornelia de Lange syndrome

Dexton Antony Johns et al. Contemp Clin Dent. 2012 Apr.

Abstract

Cornelia de Lange syndrome is a syndrome of multiple congenital anomalies. The genetic and molecular bases of these lesions are not clear. It is divided into three types based on the severity of the anomaly. Dental findings revealed contracted maxilla, malaligned teeth, multiple impacted and missing teeth. This article describes the successful management of upper central incisor with lateral opening in the apical third on the mesial surface of the root along with aesthetic and functional rehabilitation.

Keywords: Cornelia de Lange syndrome; lateral opening; mineral trioxide aggregate.

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Conflict of interest statement

Conflict of Interest: None declared.

Figures

Figure 1
Figure 1
Synophrys and long curly eyelashes
Figure 2
Figure 2
Excessive hair growth
Figure 3
Figure 3
Clinodactyly
Figure 4
Figure 4
Excessive pigmentation of palms
Figure 5
Figure 5
Excessive pigmentation of soles
Figure 6
Figure 6
Preoperative
Figure 7
Figure 7
Preoperative intraoral periapical
Figure 8
Figure 8
Post-obturation OPG
Figure 9
Figure 9
Postoperative occlusal view
Figure 10
Figure 10
Postoperative
See this image and copyright information in PMC

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