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Case Reports
. 2011 Jun;10(2):173-5.
doi: 10.1007/s12663-010-0153-1. Epub 2011 Mar 22.

Destombes-rosai dorfman disease: a rare case report

Arun Goyal  1 , Ankur Mittal
Affiliations
Case Reports

Destombes-rosai dorfman disease: a rare case report

Arun Goyal et al. J Maxillofac Oral Surg. 2011 Jun.

Abstract

Destombes Rosai Dorfman disease and sinus histocytosis with massive lymphadenopathy is a rare benign idiopathic proliferative disease of phagocytic histiocytes. Approximately 80% of patient present with painless massive cervical lymphadenopathy. It rarely involves other sites for example CNS, eyes, upper respiratory tract and skin. A case of Destombes Rosai Dorfman disease is reported with history of gradual protrusion of left eye since many years. The histological features were consistent with the diagnosis.

Keywords: Management; Orbit; Rosai dorfman disease.

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Figures

Fig. 1
Fig. 1
CT scan
Fig. 2
Fig. 2
Histopathological picture
Fig. 3
Fig. 3
a Pre op. b Post op
See this image and copyright information in PMC

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