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Case Reports
. 2012 Jun;12(3):199-201.
doi: 10.1136/practneurol-2012-000256.

Torsade de pointes in Kearns-Sayre syndrome

Stéphan Wilmin  1 , David De Bels, Sebastien Knecht, Philippe Gottignies, Marie-Dominique Gazagnes, Jacques Devriendt
Affiliations
Case Reports

Torsade de pointes in Kearns-Sayre syndrome

Stéphan Wilmin et al. Pract Neurol. 2012 Jun.

Abstract

A 47-year-old woman with Kearns-Sayre syndrome (KSS) and an implanted pacemaker for complete heart block was admitted to the intensive care unit following a cardiac arrest due to ventricular tachycardia (torsade de pointes) in the setting of QT prolongation. Complete heart blocks and ventricular tachycardia are implicated as mechanisms of sudden deaths in KSS; such patients may require pacemaker implantation and implantation of an automatic implantable cardioverter-defibrillator.

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