Skip to main page content
U.S. flag

An official website of the United States government

Dot gov

The .gov means it’s official.
Federal government websites often end in .gov or .mil. Before sharing sensitive information, make sure you’re on a federal government site.

Https

The site is secure.
The https:// ensures that you are connecting to the official website and that any information you provide is encrypted and transmitted securely.

Access keys NCBI Homepage MyNCBI Homepage Main Content Main Navigation
Case Reports
. 2012:2012:942074.
doi: 10.1155/2012/942074. Epub 2012 May 27.

Unilateral absence of the pulmonary artery incidentally found in adulthood

Cenk Aypak  1 , Hülya Yıkılkan, Zekai Uysal, Süleyman Görpelioğlu
Affiliations
Case Reports

Unilateral absence of the pulmonary artery incidentally found in adulthood

Cenk Aypak et al. Case Rep Med. 2012.

Abstract

Unilateral absence of the pulmonary artery (UAPA) or pulmonary artery agenesis is a rare congenital disorder presenting with a wide spectrum of symptoms. UAPA is usually associated with cardiac anomalies and surgically treated in childhood. We report a rare case of a 50-year-old woman who was diagnosed with left pulmonary artery agenesis without any other cardiac anomalies. Clinicians should be aware of the possibility of undiagnosed cases of UAPA in patients through a chest radiograph that suggests the diagnosis. Confirmation of the diagnosis and anatomic details can be discerned by CT scanning.

PubMed Disclaimer

Figures

Figure 1
Figure 1
Chest radiograph showing loss of volume of her left lung with displacement of the mediastinum to the left.
Figure 2
Figure 2
Thoracic CT scan revealing absence of left pulmonary artery and ipsilateral pulmonary hypoplasia.
See this image and copyright information in PMC

References

    1. Griffin N, Mansfield L, Redmond KC, et al. Imaging features of isolated unilateral pulmonary artery agenesis presenting in adulthood: a review of four cases. Clinical Radiology. 2007;62(3):238–244. - PubMed
    1. Ten Harkel AD, Blom NA, Ottenkamp J. Isolated unilateral absence of a pulmonary artery: a case report and review of the literature. Chest. 2002;122(4):1471–1477. - PubMed
    1. Komatsu Y, Hanaoka M, Ito M, et al. Unilateral absence of the pulmonary artery incidentally found after an episode of hemoptysis. Internal Medicine. 2007;46(21):1805–1808. - PubMed
    1. Bouros D, Pare P, Panagou P, Tsintiris K, Siafakas N. The varied manifestation of pulmonary artery agenesis in adulthood. Chest. 1995;108(3):670–676. - PubMed
    1. Vick GW, III, Rokey R, Huhta JC, Mulvagh SL, Johnston DL. Nuclear magnetic resonance imaging of the pulmonary arteries, subpulmonary region, and aorticopulmonary shunts: a comparative study with two-dimensional echocardiography and angiography. American Heart Journal. 1990;119(5):1103–1110. - PubMed

Publication types

LinkOut - more resources