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Case Reports
. 2011 Jul 15:2011:bcr0420114147.
doi: 10.1136/bcr.04.2011.4147.

Herlyn-Werner-Wunderlich syndrome: a rare cause of pelvic pain in adolescent girls

Ana Cristina Aveiro  1 , Victor Miranda, António Jorge Cabral, Sidónia Nunes, Filomeno Paulo, Conceição Freitas
Affiliations
Case Reports

Herlyn-Werner-Wunderlich syndrome: a rare cause of pelvic pain in adolescent girls

Ana Cristina Aveiro et al. BMJ Case Rep. .

Abstract

The Herlyn-Werner-Wunderlich syndrome is a rare congenital anomaly characterised by uterus didelphys with blind hemivagina and ipsilateral renal agenesis. It usually presents after menarche with progressive pelvic pain during menses secondary to haematocolpos. Awareness is necessary in order to diagnose and treat this disorder properly before complications occur. MRI is the preferred modality for the delineation of uterine malformation. When renal anomalies are encountered, a screening should also be made for congenital abnormalities of the reproductive tract and vice versa. The authors report a case of a girl with this condition who had a prenatal diagnose of right renal agenesis and presented at 13 years old with pelvic pain caused by haematocolpos.

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Conflict of interest statement

Competing interests None.

Figures

Figure 1
Figure 1
Selected MRI images of the pelvis and abdomen. Coronal T2-weigted images: (A) Uterus didelphys bicollis and (B) a distended and blood-filled right hemivagina (arrows). Transverse images: The haematocolpos (arrows) is slightly (C) hypointense on T2-weighted images, (D) hyperintense on T1-weighted images and (E) does not suppress on fat-suppressed T1-weighted sequences.
See this image and copyright information in PMC

References

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