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Case Reports
. 2011 Apr 1:2011:bcr0120113753.
doi: 10.1136/bcr.01.2011.3753.

Spontaneously ruptured splenic aneurysm in a young patient with Ehlers-Danlos syndrome

T Rattay  1 , A Shrivastava, D J Higman, J Francombe
Affiliations
Case Reports

Spontaneously ruptured splenic aneurysm in a young patient with Ehlers-Danlos syndrome

T Rattay et al. BMJ Case Rep. .

Abstract

The authors describe a young patient with a history of type IV vascular Ehlers-Danlos syndrome (EDS) who underwent successful treatment for a spontaneous haemorrhage from a splenic artery aneurysm, and the authors would like to remind clinicians of the mortality and morbidity associated with vascular-type EDS.

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Conflict of interest statement

Competing interests None.

Figures

Figure 1
Figure 1
CT showing the splenic artery aneurysm (arrow), haemoperitoneum and splenic infarcts.
Figure 2
Figure 2
Postoperative CT angiogram showing aneurysmal coeliac axis (arrow).
Figure 3
Figure 3
CT angiogram reconstruction depicting aneurysm of coeliac axis.
See this image and copyright information in PMC

References

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