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Case Reports
. 2012 Jun;27(2):239-42.
doi: 10.3904/kjim.2012.27.2.239. Epub 2012 May 31.

Intracranial vasculopathy in a patient with systemic sclerosis: atherosclerotic or moyamoya-like disease?

Han Na Choi, Si Hye Kim, Hyun Hee Kim, Seong-Kyu Kim, Jung-Yoon Choe, Sung-Hoon Park
Case Reports

Intracranial vasculopathy in a patient with systemic sclerosis: atherosclerotic or moyamoya-like disease?

Han Na Choi et al. Korean J Intern Med. 2012 Jun.
No abstract available

Keywords: Cerebrovascular disorder; Moyamoya disease; Scleroderma, systemic.

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Conflict of interest statement

No potential conflict of interest relevant to this article was reported.

Figures

Figure 1
Figure 1
Isolated occlusion of the left middle cerebral artery and segmental stenosis (less than 50%) of the right distal M1.
Figure 2
Figure 2
Digital substract angiography showing (A) moderate stenosis of the right proximal middle cerebral artery (MCA), and (B) left proximal MCA occlusion. (C) Collateral blood was supplied by both posterior cerebral artery, with the left side being dominant.
Figure 3
Figure 3
Radionuclide resting cerebral blood flow (rCBF) study with 600 MBq 99mTc-ECD baseline (A), and 800 MBq 99mTc-ECD after injection of 1,000 mg acetazolamide (B) by single-photon emission computed tomography (SPECT) showed no definite blood flow abnormality in the cerebral hemispheres.
See this image and copyright information in PMC

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MeSH terms