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. 2012 Jun 28:6:167.
doi: 10.1186/1752-1947-6-167.

Management strategy after diagnosis of Abernethy malformation: a case report

Caroline Dm Witjes  1 , Jan Nm Ijzermans, Anton Vonk Noordegraaf, Tc Khe Tran
Affiliations

Management strategy after diagnosis of Abernethy malformation: a case report

Caroline Dm Witjes et al. J Med Case Rep. .

Abstract

Introduction: The Abernethy malformation is a rare anomaly with a widely variable clinical presentation. Many diagnostic dilemmas have been reported. Nowadays, with the evolution of medical imaging, diagnosis can be made more easily, but management of patients with an Abernethy malformation is still open for discussion.

Case presentation: In this case study, we describe a 34-year-old Caucasian man who presented with a large hepatocellular carcinoma in the presence of an Abernethy malformation, which was complicated by the development of pulmonary arterial hypertension.

Conclusion: This case underlines the importance of regular examination of patients with an Abernethy malformation, even in older patients, to prevent complications and to detect liver lesions at an early stage.

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Figures

Figure 1
Figure 1
Magnetic resonance angiography showing hepatocellular carcinoma and a portocaval shunt.
Figure 2
Figure 2
The portocaval shunt peri-operatively.
Figure 3
Figure 3
The portocaval shunt peri-operatively.
See this image and copyright information in PMC

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