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Case Reports
. 2012:2:26.
doi: 10.4103/2156-7514.96541. Epub 2012 May 23.

CT Manifestations of Osler-Weber-Rendu Syndrome in Liver: Report of Three Cases

Qu Chuan-Qiang  1 , Guo Shou-Gang, He Yan, Chen Yu-Xin
Affiliations
Case Reports

CT Manifestations of Osler-Weber-Rendu Syndrome in Liver: Report of Three Cases

Qu Chuan-Qiang et al. J Clin Imaging Sci. 2012.

Abstract

Osler-Weber-Rendu syndrome is characterized by widespread telangiectasias. Its clinical manifestations depend on position and scope of the abnormal vessels. The clinical and CT data of 3 patients with Osler-Weber-Rendu syndrome were retrospectively analyzed. CT features reviewed include the change of volume and configuration of liver, presence of tortuous and irregular vessels, opacified vessel mass, arteriovenous shunt, and splenomegaly. CT is helpful for diagnosis, treatment, and follow-up of Osler-Weber-Rendu syndrome.

Keywords: Computed tomography; Osler-Weber-Rendu syndrome; liver; maximum intensity projection; volume rendering technique.

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Conflict of interest statement

Conflict of Interest: None declared.

Figures

Figure 1
Figure 1
CT images before surgery in Case 1. Figure 1a is coronal MIP reconstructed image in arterial phase that shows tortuous and irregular arteries in liver and portahepatis. Heterogeneity of the contrast enhancement in hepatic parenchyma with multiple opacified vessel masses is also observed. (b) VRT image shows two tortuous and distended arteries derived from the celiac trunk supplying the left and right lobes of the liver.
Figure 2
Figure 2
CT images after surgery in (a) arterial phase and (b) VRT respectively. The arteries in porta hepatis are decreased compared with those before operation.
Figure 3(a and b)
Figure 3(a and b)
CT images in arterial phase and VRT respectively in Case 2. Irregular and tortuous arteries in the liver parenchyma, and porta hepatis are present. The intra-hepatic billary ducts are dilated. Splenomegaly with gastric varices is identified.
Figure 4(a and b)
Figure 4(a and b)
CT images in arterial phase and VRT respectively in Case 3. Enlarged caudate lobe is present. Tortuous vessels are observed in the porta hepatis.
See this image and copyright information in PMC

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