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Case Reports
. 2012;67(6):693-6.
doi: 10.6061/clinics/2012(06)26.

Anesthesia in a child with Maroteaux-Lamy syndrome undergoing mitral valve replacement

Cem Sayilgan  1 , Lale Yuceyar, Sedat Akbas, Hulya Erolcay
Affiliations
Case Reports

Anesthesia in a child with Maroteaux-Lamy syndrome undergoing mitral valve replacement

Cem Sayilgan et al. Clinics (Sao Paulo). 2012.
No abstract available

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Conflict of interest statement

No potential conflict of interest was reported.

Figures

Figure 1
Figure 1
Lateral position showing kyphoscoliosis and short stature.
Figure 2
Figure 2
Coarse face - one of the confirmatory feature of Maroteaux-Lamy syndrome.
See this image and copyright information in PMC

References

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    1. Wilson CS, Mankin HT, Pluth JR. Aortic-Stenosis and Mucopolysaccharidosis. Ann Intern Med. 1980;92(4):496–8. - PubMed
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    1. Oudit GY, Butany J, Williams WG, Clarke JT, Iwanochko RM. Images in cardiovascular medicine. Left ventricular aneurysm associated with mucopolysaccharidosis type VI syndrome (Maroteaux-Lamy syndrome). Circulation. 2007;115(5):e60–2. - PubMed
    1. Oudit GY, Butany J, Williams WG, Siu SC, Clarke JT, Iwanochko RM. Left ventricular aneurysm in a patient with mucopolysaccharidosis type VI (Maroteaux-Lamy syndrome): clinical and pathological correlation. Cardiovasc Pathol. 2007;16(4):237–40. - PubMed

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