[Sclerosing epithelioid fibrosarcoma of the paravertebral column. Case report and literature review]

Abstract

Sclerosing epithelioid fibrosarcoma (SEF) is a rare variant of low-grade fibrosarcoma, with specific histological and immunohistochemical features and a poor prognosis. We report a case of SEF of the paravertebral column in a 49-year old male who presented a paraspinal mass with extension into the L4-L5 neural foramen and invasion of the L5 nerve root. Histology of the tumourectomy specimen and its immunohistochemical study led to the diagnosis of SEF. This case was particularly unusual due to its paravertebral column location and, despite its low grade, illustrates the malignant potential of SEF.

Keywords: Fibrosarcoma epitelioide esclerosante; Late metastases; Metástasis tardías; Nervous system; Paraspinal tumour; Paravertebral column tumour; Prognosis; Pronóstico; Sclerosing epithelioid fibrosarcoma; Sistema nervioso; Tumor paraespinal; Vimentin; Vimentina.