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Case Reports
. 2012 Nov;83(5):316-20.
doi: 10.4174/jkss.2012.83.5.316. Epub 2012 Oct 29.

Radical resection of intestinal blue rubber bleb nevus syndrome

Kang Kook Choi  1 , Jin Yong Kim, Min Jung Kim, Hyojun Park, Dong Wook Choi, Seong Ho Choi, Jin Seok Heo
Affiliations
Case Reports

Radical resection of intestinal blue rubber bleb nevus syndrome

Kang Kook Choi et al. J Korean Surg Soc. 2012 Nov.

Abstract

Blue rubber bleb nevus syndrome (BRBNS) is a rare systemic vascular disorder characterized by multiple venous malformations involving many organs. BRBNS can occur in various organs, but the most frequently involved organs are the skin and gastrointestinal (GI) tract. GI lesions of BRBNS can cause acute or chronic bleeding, and treatment is challenging. Herein, we report a case of GI BRBNS that was successfully treated with a combination of intraoperative endoscopy and radical resection.

Keywords: Bleeding; Blue rubber bleb nevus syndrome; Hemorrhage; Intestines.

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Conflict of interest statement

No potential conflict of interest relevant to this article was reported.

Figures

Fig. 1
Fig. 1
A 0.5 cm hemangioma was found in the sigmoid colon without evidence of bleeding on colonoscopy.
Fig. 2
Fig. 2
The small intestine was explored to the proximal jejunum, and three hemangiomas were found. Two hemangiomas had mucosal erosions. (A) The most proximal hemangioma was located in the duodenojejunal junction. (B) The middle hemangioma. (C) The most distal hemangioma was found in the proximal jejunum.
Fig. 3
Fig. 3
(A) The tattoo performed via double-balloon endoscopy was observed. (B, C) Four other hemangiomas were identified distal to the tattooed point of the intestine. (D) Segmental resection and end-to-end anastomosis were performed for two segments that had two hemangiomas in close proximity.
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