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Case Reports
. 2012 Sep;3(3):208-10.
doi: 10.4103/2229-5178.101823.

Extensive morphea profunda with autoantibodies and benign tumors: A rare case report

Affiliations
Case Reports

Extensive morphea profunda with autoantibodies and benign tumors: A rare case report

Leelavathy Budamakuntla et al. Indian Dermatol Online J. 2012 Sep.

Abstract

The term deep morphea describes a variant of morphea (localised scleroderma) in which inflammation and sclerosis are found in the deep dermis, panniculus, fascia or superficial muscle. It is sometimes associated with autoantibodies. We report the case of a 49 year-old male who had morphea profunda (radiologically and histopathologically confirmed) affecting mainly the left side of the body with face, trunk and limb involvement, along with autoantibody production and associated neurofibromas and lipomas.

Keywords: Autoantibodies; benign tumors; morphea profunda.

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Conflict of interest statement

Conflict of Interest: None declared.

Figures

Figure 1
Figure 1
Left-sided hemiatrophy of the face with hyperpigmented patches and swelling over the right side of the forehead
Figure 2
Figure 2
Multiple hyperpigmented atrophic patches over the left side of the back with few patches over the upper limbs
Figure 3
Figure 3
Hyperpigmented atrophic patches over the left upper limb, inframammary area and abdomen
Figure 4
Figure 4
(Haematoxylin and Eosin, 40X) Subcutaneous fat invaded by fibrous tissue

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