Recurrent dislocation of the patella in kabuki make-up syndrome

Abstract

Two patients with Kabuki make-up syndrome with bilateral recurrent dislocation of the patella are presented. They had generalized ligamentous laxity and patellofemoral dysplasia. Both developed patellar dislocation in adolescence and required surgery, with medial transfer of the tibial tuberosity associated with vastus medialis plasty (Insall technique). One postoperative complication occurred in one case: a nondisplaced tibia fracture at the sixth postoperative week that healed with conservative means. Final results were good in both cases. Good surgical results can be achieved in patellar dislocation in patients with Kabuki syndrome.

Figure 1

Top: CT-scan of both knees performed at the age of 15 years, showing bilateral patellofemoral dysplasia and permanent subluxation of patella. Bottom: distance TT-TG (tibial tubercle-trochlear groove) of 19 and 27 mm at the left and right side, respectively.

Figure 2

Postoperative radiograph of the knee after medial tibial tubercle transfer and vastus medialis plasty. The patella is better centred.

Figure 3

Pre- (left) and postoperative (right) radiograph of the left knee after medial and distal tibial tubercle transfer and vastus medialis plasty. The patella is better centred.