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. 2008 Mar;11(1):22-5.
doi: 10.1016/j.jus.2007.12.002. Epub 2008 Feb 8.

US, CT and MRI findings in a case of diffuse lymphangiomatosis and cystic hygroma

A Ozel  1 , E Uysal, A I Dokucu, S M Erturk, M Basak, V Cantisani
Affiliations

US, CT and MRI findings in a case of diffuse lymphangiomatosis and cystic hygroma

A Ozel et al. J Ultrasound. 2008 Mar.

Abstract
in English, Italian

Lymphangiomatosis is a rare disease with multifocal lymphatic proliferation that typically occurs during childhood and involves multiple parenchymal organs including the lung, liver, spleen, bone, and skin. Lymphangiomatosis may occur synchronously or metachronously with cystic hygroma of the neck. We present US, CT, and MRI findings of cystic hygroma of the neck associated with generalized lymphangiomatosis affecting bones and spleen in a 2-year-old girl.

SommarioLa linfangiomatosi è una rara malattia caratterizzata da proliferazione multifocale del sistema linfatico che colpisce tipicamente i soggetti giovani e può interessare molti organi parenchimali tra cui il polmone, il fegato, la milza, le ossa e la pelle. La linfangiomatosi si può associare in sincronia o successivamente con l'igroma cistico del collo. Qui di seguito sono riportati i reperti ecografici, TC e di RM, di una bimba di 2 anni con igroma cistico del collo associato con linangiomatosi generalizzata delle ossa e della milza.

Keywords: CT findings; Cystic hygroma; Lymphangiomatosis; MRI findings; US findings.

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Figures

Fig. 1
Fig. 1
Coronal sonogram shows multiple anechoic cysts in the splenic parenchyma.
Fig. 2
Fig. 2
Contrast enhanced CT shows multiple non-enhanced well defined hypodense lesions. Some small round hypodense lesions in the vertebral body are also evident.
Fig. 3
Fig. 3
Coronal T2-WI shows enlarged spleen with multiple hyperintense cysts. In the left side of the neck, there is a multiloculated hyperintense lesion with multiple hypointense septal structures. Note also small hyperintense cystic foci in the thoracic and lumbar part of the spine, and in the ribs of the left hemithorax.
Fig. 4
Fig. 4
In the cut section parallel to the long axis of a 12 × 7 × 5 cm sized spleen, numerous cysts of varying sizes filled with gelatinous material were seen.
See this image and copyright information in PMC

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