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. 2013:2013:747431.
doi: 10.1155/2013/747431. Epub 2013 Jan 3.

Cerebral venous thrombosis revealing primary sjögren syndrome: report of 2 cases

A Mercurio  1 , M Altieri, V M Saraceni, T Paolucci, G L Lenzi
Affiliations

Cerebral venous thrombosis revealing primary sjögren syndrome: report of 2 cases

A Mercurio et al. Case Rep Med. 2013.

Abstract

Sjögren syndrome (SS) is an autoimmune disease of the exocrine glands, characterized by focal lymphocytic infiltration and destruction of these glands. Neurologic complications are quite common, mainly involving the peripheral nervous system (PNS). The most common central nervous system (CNS) manifestations are myelopathy and microcirculation vasculitis. However, specific diagnostic criteria for CNS SS are still lacking. We report two cases of primary SS in which the revealing symptom was cerebral venous thrombosis (CVT) in the absence of genetic or acquired thrombophilias.

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Figures

Figure 1
Figure 1
Patient 1: MRI revealed a left parietal hematoma, while the MR venography (MRV) showed an ipsilateral TS thrombosis.
Figure 2
Figure 2
Patient 2: MRI showed a left temporal hematoma while the MRV revealed a left TS thrombosis.
See this image and copyright information in PMC

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