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Case Reports
. 2012 Jan;2(1):63-5.
doi: 10.4103/2231-0746.95324.

Palatoplasty in a patient with Seckel syndrome

Ramneesh Garg  1 , Sanjeev Uppal, Rajinder Mittal, Anju Grewal, Dinesh Sood, Sheerin Shah
Affiliations
Case Reports

Palatoplasty in a patient with Seckel syndrome

Ramneesh Garg et al. Ann Maxillofac Surg. 2012 Jan.

Abstract

We report a rare case of a patient of Seckel syndrome having cleft palate born to nonconsanguineous married parents. This 8-year-old male child underwent successful palatoplasty under general anesthesia. Till date there are approximately 60 cases of Seckel syndrome reported in the literature. The syndrome which has autosomal recessive inheritance is characterized by Intra Uterine Growth Retardation, microcephaly, dwarfism, and bird-like face. The associated features of the syndrome and technical details of surgery and anesthesia are discussed.

Keywords: Cleft palate; Seckle syndrome; palatoplasty.

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Conflict of interest statement

Conflict of Interest: None declared.

Figures

Figure 1
Figure 1
Typical features of Seckle syndrome
Figure 2
Figure 2
Showing cleft palate
Figure 3
Figure 3
Height of child
Figure 4
Figure 4
Postoperative picture
See this image and copyright information in PMC

References

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