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Case Reports
. 2013 Apr 18:8:101.
doi: 10.1186/1749-8090-8-101.

Video-assisted thoracoscopic surgery for recurrent pneumothorax in pulmonary lymphangioleimyomatosis with tuberous sclerosis complex

Chia-Fen Tsai  1 , Chen-Hao Hsiao, Jang-Ming Lee, Ke-Cheng Chen, Ming-Jium Shieh, Hong-Shiee Lai, Jin-Shing Chen
Affiliations
Case Reports

Video-assisted thoracoscopic surgery for recurrent pneumothorax in pulmonary lymphangioleimyomatosis with tuberous sclerosis complex

Chia-Fen Tsai et al. J Cardiothorac Surg. .

Abstract

Pneumothorax in pulmonary lymphangioleiomyomatosis (LAM) with tuberous sclerosis complex (TSC) is a difficult condition to manage. Video-assisted thoracoscopic surgery (VATS) may play a role in diagnosis and treatment of this situation. We present a case of right recurrent pneumothorax due to LAM with TSC in whom VATS was performed for pathological diagnosis and mechanical pleurodesis. The unique presentation of LAM in TSC was also discussed.

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Figures

Figure 1
Figure 1
Images of the patient. a) sebaceous adenoma on the face, b) right ventricular subependymal giant cell astrocytoma, c) liver hamartoma and d) bilateral renal angiomyolipoma revealed by the magnetic resonance imaging (MRI).
Figure 2
Figure 2
Chest plain film showed right pneumothorax with cystic change.
Figure 3
Figure 3
a and b Chest HRCT. HRCT showed bilateral numerous cystic lesions with right small pulmonary nodules.
Figure 4
Figure 4
a and b VATS pictures. During VATS operation, a significant quantity of 2- to 3-mm diameter small cysts at the lung parenchyma and tonal change in the pleura were noted.
See this image and copyright information in PMC

References

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