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Case Reports
. 2013 Apr 19:2013:bcr2013008800.
doi: 10.1136/bcr-2013-008800.

Challenges in orthopaedic management of Parkes-Weber syndrome

Mara Silva Ferreira  1 , Telma Francisco, Delfin Tavares
Affiliations
Case Reports

Challenges in orthopaedic management of Parkes-Weber syndrome

Mara Silva Ferreira et al. BMJ Case Rep. .

Abstract

A 16-year-old boy with a diagnosis of Parkes-Weber syndrome presented with a lower leg discrepancy of 3 cm for orthopaedic management. He had the triad of red skin lesion, lymphoedema and overgrowth of the right leg and multiple arteriovenous fistulae confirmed by angiography. Considering the risk of aggravating the vascular lesion, we decided conservative management of unequal limb lengths as long as this is well tolerated.

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Figures

Figure 1
Figure 1
Lower limb MRI showing dilated vascular structures in the right lower limb involving subcutaneous and multiple muscle compartments, flow voids consistent with arteriovenous malformation and subcutaneous oedema.
Figure 2
Figure 2
Hypertrophy and trophic cutaneous lesions of the right lower limb.
Figure 3
Figure 3
Hypertrophy of muscles and bones of the right lower limb, with discrepancy of 3 cm.
See this image and copyright information in PMC

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