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Review

. 2013 May 1;187(9):915-9.

doi: 10.1164/rccm.201301-0184UP.

Update in cystic fibrosis 2012

Christopher H Goss¹, Felix Ratjen

Affiliations

PMID: 23634859
PMCID: PMC5448509
DOI: 10.1164/rccm.201301-0184UP

Review

Update in cystic fibrosis 2012

Christopher H Goss et al. Am J Respir Crit Care Med. 2013.

. 2013 May 1;187(9):915-9.

doi: 10.1164/rccm.201301-0184UP.

Authors

Christopher H Goss¹, Felix Ratjen

Affiliation

¹ Division of Pulmonary and Critical Care Medicine, Department of Medicine, University of Washington, Seattle, WA, USA. goss@u.washington.edu

PMID: 23634859
PMCID: PMC5448509
DOI: 10.1164/rccm.201301-0184UP

No abstract available

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References

1. Cystic Fibrosis Foundation. Bethesda, MD: Cystic Fibrosis Foundation; 2011. Patient registry: Annual data report 2010.
1. Pezzulo AA, Tang XX, Hoegger MJ, Alaiwa MH, Ramachandran S, Moninger TO, Karp PH, Wohlford-Lenane CL, Haagsman HP, van Eijk M, et al. Reduced airway surface pH impairs bacterial killing in the porcine cystic fibrosis lung. Nature. 2012;487:109–113. - PMC - PubMed
1. Mou H, Zhao R, Sherwood R, Ahfeldt T, Lapey A, Wain J, Sicilian L, Izvolsky K, Musunuru K, Cowan C, et al. Generation of multipotent lung and airway progenitors from mouse ESCs and patient-specific cystic fibrosis iPSCs. Cell Stem Cell. 2012;10:385–397. - PMC - PubMed
1. Wong AP, Bear CE, Chin S, Pasceri P, Thompson TO, Huan LJ, Ratjen F, Ellis J, Rossant J. Directed differentiation of human pluripotent stem cells into mature airway epithelia expressing functional CFTR protein. Nat Biotechnol. 2012;30:876–882. - PMC - PubMed
1. Goddard AF, Staudinger BJ, Dowd SE, Joshi-Datar A, Wolcott RD, Aitken ML, Fligner CL, Singh PK. Direct sampling of cystic fibrosis lungs indicates that DNA-based analyses of upper-airway specimens can misrepresent lung microbiota. Proc Natl Acad Sci USA. 2012;109:13769–13774. - PMC - PubMed

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