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. 2013 Dec;21(12):561-4.
doi: 10.1007/s12471-013-0426-7.

A calcified sinutubular junction: the discovery of a supravalvular aortic stenosis in an elderly woman

L Cozijnsen  1 , M Bakker-de Boo, J J Kardux, B J Bouma
Affiliations

A calcified sinutubular junction: the discovery of a supravalvular aortic stenosis in an elderly woman

L Cozijnsen et al. Neth Heart J. 2013 Dec.

Abstract

We report a case of a 64 year old woman with a calcified ring at the level of the sinotubular junction. Echocardiography and Computed Tomography showed a supravalvular aortic stenosis, without known associated lesions, except for the existence of an aberrant right subclavian artery. These combination of abnormalities makes it an unique case. Differential diagnosis of sinutubular calcification is added. From the literature a short review of supravalvular aortic stenosis is presented with indications for surgical intervention. Lifelong and regular follow up is necessary.

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Figures

Fig. 1
Fig. 1
Cardiac echocardiography with apical views demonstrating the SVAS (a, left, arrow). Pulsed-wave Doppler measurement shows a maximal velocity of 1.8 m/s across the stenosis (b, middle). Colour Doppler visualises the turbulence at the level of the ST junction (c, right)
Fig. 2
Fig. 2
CT images in a three-chamber plane. Thick (a, left) and thin (b, right) slice maximum intensity projection (MIP) reconstructions, visualising the calcified ST ridge
Fig. 3
Fig. 3
CT MIP reconstructions. Axial-oblique plane (a, left) showing the calcified ring (arrow, SVAS) and axial plane (b, right) showing the aberrant right subclavian artery (arrow, LUSORIA) originating from the distal arcus aortae (arrow, ARCUS)
See this image and copyright information in PMC

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