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Case Reports
. 2013 Jan;6(1):41-4.
doi: 10.4103/0974-2077.110098.

Extensive Invasive Extramammary Paget's Disease: Surgical Treatment

Uwe Wollina  1
Affiliations
Case Reports

Extensive Invasive Extramammary Paget's Disease: Surgical Treatment

Uwe Wollina. J Cutan Aesthet Surg. 2013 Jan.

Abstract

Extramammary Paget's disease is uncommon. Diagnosis has to be confirmed by histopathology. Treatment is a challenge in cases with extended tumors. We present a 70-year-old male patient with extensive genitoanal Paget's disease. Mohs surgery is the gold standard in such cases. Details of the surgical planning are discussed including wound bed preparation. Radiotherapy may be an alternative.

Keywords: Apocrine malignancy; Extramammary Paget's disease; Mohs surgery; transplantation.

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Conflict of interest statement

Conflict of Interest: None declared.

Figures

Figure 1
Figure 1
Clinical aspect of extensive extramammary invasive Pagetæs disease with involvement of groins scrotum and perineum
Figure 2a
Figure 2a
Surgical situs after Mohs surgery
Figure 2b
Figure 2b
The excised tumor
Figure 3
Figure 3
Histopathology of the tumor with pagetoid cell proliferations and invasive growth (H and E, ×4)
Figure 4
Figure 4
Mesh-graft split skin transplantation after induction of granulation by topical CO2
Figure 5
Figure 5
Good functional and esthetic outcome
See this image and copyright information in PMC

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