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. 2013:2013:758416.
doi: 10.1155/2013/758416. Epub 2013 Jun 13.

Multifocal adult rhabdomyoma of the head and neck manifestation in 7 locations and review of the literature

Lorraine A de Trey  1 , Stephan Schmid, Gerhard F Huber
Affiliations

Multifocal adult rhabdomyoma of the head and neck manifestation in 7 locations and review of the literature

Lorraine A de Trey et al. Case Rep Otolaryngol. 2013.

Abstract

Background. Adult rhabdomyoma is a rare benign tumour with the differentiation of striated muscle tissue, which mainly occurs in the head and neck region. Twenty-six cases of multifocal adult rhabdomyoma are documented in the literature. Method. We report a 55-year-old male with simultaneous diagnosis of 7 adult rhabdomyomas and review the literature of multifocal adult rhabdomyoma. Result. Review of the literature revealed 26 cases of multifocal adult rhabdomyoma, of which only 7 presented with more than 2 lesions. Mean age at diagnosis was 65 years with a male to female ratio of 5.5 : 1. Common localizations were the parapharyngeal space (36%), larynx (15%), submandibular (14%), paratracheal region (12%), tongue (11%), and floor of mouth (9%). Besides the known radiological features of adult rhabdomyoma, our case showed FDG-uptake in (18) F-FDG PET/CT. Conclusion. This is the first case of multifocal adult rhabdomyoma published, with as many as 7 simultaneous adult rhabdomyomas of the head and neck.

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Figures

Figure 1
Figure 1
MRI ARM parapharyngeal space with submandibular extension.
Figure 2
Figure 2
Laryngoscopy (inspiration and phonation) with left paraglottic ARM.
Figure 3
Figure 3
Right parapharyngeal ARM after excision.
See this image and copyright information in PMC

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