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. 2011 Jul;23(3):151-3.
doi: 10.1016/j.jsha.2011.01.010. Epub 2011 Jan 13.

Pulmonary atresia with hypoplastic right ventricle and large subaortic ventricular septal defect

Muhammad Arif Khan  1 , Mohammed Omar Galal
Affiliations

Pulmonary atresia with hypoplastic right ventricle and large subaortic ventricular septal defect

Muhammad Arif Khan et al. J Saudi Heart Assoc. 2011 Jul.

Abstract

A neonate is presented with a very rare association consisting of pulmonary atresia with large ventricular septal defect but additionally, combined with a hypoplastic right ventricle and well developed pulmonary arteries. The management strategy is described.

Keywords: Hypoplastic right ventricle; Normal pulmonary arteries; Pulmonary atresia; Ventricular septal defect.

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Figures

Figure 1
Figure 1
Subcostal view showing PFO with right to left shunt. PFO, patent foramen ovale; RA, right atrium; LA, left atrium.
Figure 2
Figure 2
Parasternal short axis view showing pulmonary atresia with confluent PA, of reasonable diameters. PV, pulmonary valve; RPA, right pulmonary artery; LPA, left pulmonary artery.
Figure 3
Figure 3
Subcostal view showing malaligned ventricular septal defect as well as hypoplastic right ventricle opening into aorta. RV, right ventricle; LV, left ventricle; Ao, Aorta.
Figure 4
Figure 4
Subcostal view with colour showing malaligned ventricular septal defect as well as hypoplastic right ventricle opening into aorta.
Figure 5
Figure 5
Subcostal view showing hypoplastic tricuspid valve and hypoplastic right ventricle.. RA, right atrium; RV, right ventricle.
Figure 6
Figure 6
Suprasternal short axis view showing normal arch with large PDA.
See this image and copyright information in PMC

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References

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