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. 2012 Mar 9;4(1):295-306.
doi: 10.3390/cancers4010295.

Desmoid tumors in the pediatric population

Joshua N Honeyman  1 , Michael P La Quaglia
Affiliations

Desmoid tumors in the pediatric population

Joshua N Honeyman et al. Cancers (Basel). .

Abstract

Desmoid tumors are benign soft tissue tumors associated with locally aggressive growth and high rates of morbidity, but they do not metastasize via lymphatic or hematogenous routes. While most of the data on desmoid tumors originates in the adult literature, many of the findings have been applied to the management of pediatric patients. This article discusses the epidemiology, etiology, clinical presentation, pathology, and treatment of this rare tumor in the pediatric population and includes a literature review of the most recent large series of pediatric patients with desmoid tumors.

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Figures

Figure 1
Figure 1
The microscopic appearance of a desmoid tumor reveals well-differentiated cells and bands of fibrous tissue.
Figure 2
Figure 2
T1 (a) and T2 (b) weighted MRI and contrast-enhanced CT (c) of desmoid tumors provide anatomic information useful in the management of desmoid tumors.
See this image and copyright information in PMC

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