Epidemiology of pulmonary arterial hypertension

Abstract

Changes in the epidemiology of pulmonary arterial hypertension (PAH) have resulted from changes in classification schemes and an increased emphasis on diagnosis because of the availability of effective therapies. The terms primary pulmonary hypertension and secondary pulmonary hypertension are considered inappropriate, confusing, and should not be used. Recent registries of patients with PAH have provided improved data regarding prognosis in the era of advanced therapies.

Keywords: Anorectic drugs; HIV infection; Hemolytic anemia; Idiopathic pulmonary arterial hypertension; Portopulmonary hypertension; Pulmonary arterial hypertension; Pulmonary veno-occlusive disease; Systemic sclerosis.