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Case Reports
. 2013 Oct;5(4):296-8.
doi: 10.4103/0974-7796.120299.

Prune belly syndrome with urethral hypoplasia and vesico-cutaneous fistula: A case report and review of literature

Osama M Sarhan  1 , Mustafa S Al-Ghanbar, Ziad M Nakshabandi
Affiliations
Case Reports

Prune belly syndrome with urethral hypoplasia and vesico-cutaneous fistula: A case report and review of literature

Osama M Sarhan et al. Urol Ann. 2013 Oct.

Abstract

Association between Prune belly syndrome (PBS) and urethral hypoplasia is an unusual condition. It is usually fatal unless there is a communication between the fetal bladder and the amniotic sac. We report a case of PBS with urethral hypoplasia and congenital vesico-cutaneous fistula in a male neonate. Patient underwent cutaneous vesicostomy and was discharged for close follow up of his renal function and for future reconstruction.

Keywords: Prune belly syndrome; urethral hypoplasia; vesico-cutaneous fistula; vesicostomy.

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Conflict of interest statement

Conflict of Interest: None.

Figures

Figure 1
Figure 1
Prune Belly syndrome patient with bilateral undescended testes and urine dribbling from a suprapubic vesico-cutaneous fistula below the urachus
Figure 2
Figure 2
Postoperative picture showing a wide cutaneous vesicostomy
Figure 3
Figure 3
Voiding cystourethrogram through the vesicostomy revealed adequate bladder capacity with bilateral high grade VUR, dilated posterior urethra and atretic anterior urethra
See this image and copyright information in PMC

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