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Case Reports
. 2013 Nov;23(6):456-9.
doi: 10.4103/0971-4065.120346.

Chronic type B aortic dissection in association with Hemolyticuremic syndrome in a child

D N Gera  1 , P P Ghuge, S Gandhi, A V Vanikar, J D Shrimali, V B Kute, H L Trivedi
Affiliations
Case Reports

Chronic type B aortic dissection in association with Hemolyticuremic syndrome in a child

D N Gera et al. Indian J Nephrol. 2013 Nov.

Abstract

Aortic dissection (AD) is a potentially life-threatening medical emergency usually encountered in the elderly. Here, we report a 9-year-old child who was incidentally detected to have asymptomatic chronic type B dissecting aneurysm of aorta when he presented with relapse of Hemolytic uremic syndrome (HUS) without any genetic abnormalities like Marfan or Ehler-Danlos syndrome. To the best of our knowledge, this is the first case of AD associated with HUS in a child without any known associated genetic or inherited risk factors.

Keywords: Child; dissecting aneurysm of aorta; hemolytic uremic syndrome; hypertension.

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Conflict of interest statement

Conflict of Interest: None declared.

Figures

Figure 1
Figure 1
X-ray chest on initial admission and at the time of relapse of Hemolytic uremic syndrome, second X-ray shows well-defined soft-tissue opacity in left paratracheal and left paracardiac region and shadow of aortic knob and descending aorta not visualized
Figure 2
Figure 2
Doppler study - Longitudinal section view showing dissection flap within aorta separating true lumen and false lumen and peripheral thrombus in true lumen
Figure 3
Figure 3
Computed tomography angio of coronal and axial view-showing normal ascending aorta, dissection starting after left subclavian artery extending up to bifurcation of the aorta with dissection flap and peripheral thrombus in true lumen
Figure 4
Figure 4
3D representation of aorta showing dissection starting after left subclavian artery extending to bifurcation of the aorta with the site of intimal flap and renal arteries of normal caliber on both sides (left side two renal arteries, right side one renal artery)
Figure 5
Figure 5
Glomeruli show wrinkled and duplicated basement membranes and congested capillary lumina with red blood cells and fibrin thrombi. Interlobular artery shows marked mucointimal proliferation with subintimal focal fibrin deposition
See this image and copyright information in PMC

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